JKMC | VOL. 5 | NO. 4 | ISSUE 18 | OCT-DEC, 2016

Isolated intestinal ganglioneuromatosis - A rare entity
Laudari U, Rupakheti S, Bohara TP, Joshi MR, Lakhey M


Intestinal ganglioneuromatosis are rare benign tumour of ganglionic cell origin, most of them associated with neurofibromatosis type I and multiple endocrine neoplasia type IIB. They are benign tumours with rare malignant transformation, have a varied clinical presentation and long indolent course. Surgical resection is the only modality of treatment and diagnosis is based on histopathological examination and immunohistochemistry. We report a case, 55 year old male who was diagnosed as a case of isolated intestinal ganglioneuromatosis, i.e no association with neurofi bromatosis type I and multiple endocrine neoplasia type IIB. He is on regular follow up with normal daily activities and no evidence of recurrence.

Keyword : Ganglioneuromatosis, Small Intestine